Can Mpnst Be Cured

Malignant peripheral nerve sheath tumors (MPNST) are aggressive soft tissue sarcomas characterized by high risk of local recurrence and distant metastasis. The only known curative therapy is complete resection.

How common is Mpnst?

MPNST is most common in young adults and middle-aged adults. MPNST is more common in people with a genetic condition called neurofibromatosis type 1 (NF1). About 25% to 50% of people with MPNST have NF1. And about 8% to 13% of people with NF1 will get MPNST in their lifetime.

How is Mpnst treated?

The conventional treatment for MPNST involves surgical resection. Adjuvant radiation therapy is generally recommended for patients with large high-grade lesions (>5 cm) or with positive resected tumor margins.